Names | |
---|---|
IUPAC name
3-[5-(Aminomethyl)-4-(carboxymethyl)-1H-pyrrol-3-yl]propanoic acid
|
|
Identifiers | |
3D model (JSmol)
|
|
ChemSpider | |
DrugBank | |
ECHA InfoCard | 100.006.970 |
EC Number | 207-666-3 |
MeSH | Porphobilinogen |
PubChem CID
|
|
UNII | |
|
|
|
|
Properties | |
C10H14N2O4 | |
Molar mass | 226.229 |
Except where otherwise noted, data are given for materials in their standard state (at 25 °C [77 °F], 100 kPa).
|
|
what is ?) | (|
Infobox references | |
Porphobilinogen (PBG) is a pyrrole involved in porphyrin metabolism.
It is generated from aminolevulinate (ALA) by the enzyme ALA dehydratase. PBG is then converted into hydroxymethyl bilane by the enzyme porphobilinogen deaminase, also known as hydroxymethylbilane synthase.
Acute intermittent porphyria causes an increase in urinary porphobilinogen.